Bone and soft tissue tumors

Epithelioid sarcoma is more common in men than in women, and tends to occur in young adults between 20 and 40 years old. It is rare in children and the elderly, but it can occur at any age.

According to the location of occurrence, it is divided into distal type (that is, classic, mainly located at the end of the limbs) and proximal type (occurring in the head, neck and trunk), with the former being more common. The distal type is more common in the wrist, and the tumor is manifested as slow growing nodules or plaques, such as invasion of the dermis, which may cause ulcers. In the advanced stage, the lesions may be manifested as linear ulcerative nodules, usually <5 cm in diameter, spreading along the blood vessels, nerves and fascia, such as involving large nerves, pain, paresthesia and even muscle atrophy. The onset of proximal epithelioid sarcoma is older, usually deep multiple soft tissue masses, larger in volume, the largest of up to 20 cm in diameter, are most likely to occur in the head and neck, pelvic area, groin area, perineal anal area, external genital area, etc. Those who occur in the pelvic area are often prone to compression symptoms. Although epithelioid sarcoma is a low-grade malignant tumor, extensive or radical resection is recommended due to early lymph node and lung metastasis.